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Masaharu Kotani Selected Research

Masaharu Kotani Research Topics

Disease

6Fabry Disease (Fabry's Disease)
10/2006 - 12/2002
3Mucolipidoses (Sialidosis)
03/2007 - 06/2004
2Neuraminidase deficiency with beta-galactosidase deficiency
04/2006 - 06/2004
2Carcinoma (Carcinomatosis)
09/2003 - 02/2003
1Edema (Dropsy)
05/2015
1Brain Edema (Cerebral Edema)
05/2015
1Epilepsy (Aura)
05/2015
1Seizures (Absence Seizure)
05/2015
1Status Epilepticus (Complex Partial Status Epilepticus)
05/2015
1Cardiomyopathies (Cardiomyopathy)
10/2006
1Neuraminidase 1 deficiency
04/2006
1Lysosomal Storage Diseases (Lysosomal Storage Disease)
04/2006
1Nonaka type Distal myopathy
04/2005
1Sandhoff Disease (Sandhoff's Disease)
01/2005
1Neuroblastoma
07/2004
1Nervous System Diseases (Neurological Disorders)
01/2004
1Type I Schindler Disease
01/2004
1Inborn Genetic Diseases (Disease, Hereditary)
01/2004
1Neuroaxonal Dystrophies (Neuroaxonal Dystrophy, Late Infantile)
01/2004
1GM2 Gangliosidoses (GM2 Gangliosidosis)
01/2002

Drug/Important Bio-Agent (IBA)

5EnzymesIBA
03/2007 - 12/2002
4alpha-Galactosidase (Beano)IBA
10/2006 - 12/2002
3LectinsIBA
03/2007 - 06/2004
3GlycoconjugatesIBA
03/2007 - 01/2004
3Glycoproteins (Glycoprotein)IBA
04/2006 - 12/2002
2Mannose (D-Mannose)IBA
03/2007 - 01/2006
2SugarsIBA
03/2007 - 12/2002
1Levetiracetam (Keppra)FDA LinkGeneric
05/2015
1Diazepam (Valium)FDA LinkGeneric
05/2015
1Pilocarpine (Ocusert)FDA LinkGeneric
05/2015
1G(M2) Ganglioside (Ganglioside GM2)IBA
03/2007
1Monoclonal AntibodiesIBA
03/2007
1Phospholipids (Phosphatides)FDA LinkGeneric
10/2006
1sialooligosaccharidesIBA
04/2006
1Cathepsin AIBA
04/2006
1Neuraminidase (Sialidase)IBA
04/2006
1Complementary DNA (cDNA)IBA
04/2006
1Peptide-N4-(N-acetyl-beta-glucosaminyl) Asparagine AmidaseIBA
04/2006
1Proteins (Proteins, Gene)FDA Link
04/2006
1Fluorescein-5-isothiocyanate (FITC)IBA
04/2006
1beta-Galactosidase (Lactaid)IBA
04/2006
15'-deoxy-5'-phosphonomethyladenosine phosphateIBA
04/2006
1AvidinIBA
04/2006
1mannose-6-phosphateIBA
01/2006
1agalsidase betaFDA Link
01/2006
1Bovine Serum AlbuminIBA
01/2006
1agalsidase alfaIBA
01/2006
1Polysaccharides (Glycans)IBA
04/2005
1Tyrosine (L-Tyrosine)FDA Link
07/2004
1Tn antigenIBA
01/2004
1alpha-N-Acetylgalactosaminidase (N-Acetyl-alpha-D-Galactosaminidase)IBA
01/2004
1Membrane Glycoproteins (Membrane Glycoprotein)IBA
09/2003
1AntigensIBA
09/2003
1GangliosidesIBA
02/2003
1Tretinoin (Retinoic Acid)FDA LinkGeneric
02/2003
1alpha-Mannosidase (LAMAN)IBA
12/2002
1beta-N-AcetylhexosaminidasesIBA
01/2002

Therapy/Procedure

4Enzyme Replacement Therapy
01/2006 - 12/2002
2Therapeutics
01/2005 - 12/2002